The partial ventricular atrioventricular canal is a cardiac malformation. In almost all cases, the elementary anomaly of the atrioventricular valve, tripled by “mitral cleft”, is associated with it while the right atrioventricular valve is either normal, tricuspid, or lacunar between its anterior and septal valves. It accounts for about 3% of all cardiac malformations   . It is present in two cases out of 10,000 live births. Both sexes are also affected, with a slightly higher frequency among women (F/H ratio at 1.3). The diagnosis of a partial ventricular atrioventricular canal at age 73 is not a common situation.
We report the case of a 73-year-old patient who consulted for a global heart failure syndrome. He has no known cardiovascular history, but has been symptomatic of a global heart failure since the age of 18 with periods of remission. The initial assessment, in particular the electrocardiogram and the Doppler echo, could not be performed for financial difficulties. The current episode dates from 03/07/2018 marked by a dyspnea of increasing evolution, a cough with whitish sputum and edema of the lower limbs. The cardiovascular examination found irregular heart sounds at times, a 3/6 systolic murmur at the mitral focus and a blood pressure of 110/80mmmHg. The arterial distension was well perceived. Pulmonary auscultation revealed cerebral crackles at both pulmonary bases. The abdominal examination found painful hepatomegaly associated with hepatic jugular reflux. The biological assessment (glycemia, serum creatinine, blood ionogram, TSHus, HIV serology) was unremarkable and the blood count and count showed anemia at 7 g/dl. The electrocardiogram recorded complete arrhythmia with atrial fibrillation associated with a straight bundle of branches (Figure 1). The frontal chest X-ray showed cardiomegaly associated with vascular redistribution to the apex (Figure 2).
The cardiac Doppler echo revealed a large axis of the sternal axis with a mitral cleft associated with severe mitral insufficiency (Figure 3). In four cavities, a large ostium primum interatrial communication was shown (Figure 4). This interatrial communication and bi-atrial dilation were best seen in the xiphoidal section (Figure 5).
Figure 1. Electrocardiogram.
Figure 2. Frontal chest X-ray.
Figure 3. The cardiac Doppler echo revealed a large axis of the sternal axis with a mitral cleft associated with severe mitral insufficiency.
Figure 4. Four cavity cut showing biatrial dilatation and interatrial communication.
Figure 5. Costal cut showing ostium primum inter atrial communication.
The evolution was marked by the regression of the symptomatology of cardiac insufficiency under a conventional treatment associating a reduced diet, of diuretic, of the inhibitor of conversion enzyme and of an anti vitamin K and a transfusion of 3 pockets fresh blood. The treatment was medical due to lack of technical platform and the high cost of evacuation to a more equipped center outside the country.
The peculiarity of this clinical case is mainly related to its mode of symptomatic discovery at the age of 18 years. According to literature, tolerance is generally excellent during the first years of life. It is very rare but possible that a massive left atrioventricular leak puts the patient in cardiac insufficiency so obvious as to wonder about the operative indication from the earliest childhood. But more often and more rapidly than in other atrial septal defects, in the course of the second childhood or adolescence, we end up seeing heart failure or rhythm disturbances, which leads to the operative indication  . The diagnosis of the partial atriventricular canal was evoked in front of a global cardiac insufficiency, suspected from the results of the electrocardiogram and the radiography of the frontal pulmonary and confirmed by the Doppler echo as described in the works of Calabrò  We conclude that this heart failure should prompt us to pay more attention to the search for aged congenital heart disease in elderly patients. The evolution was marked by the regression of the symptomatology of heart failure until today under medical treatment.
The partial atrioventricular canal is manifested very early by global heart failure. Its prognosis is better until adolescence and rare in adulthood. The treatment is surgical.