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 JBM  Vol.4 No.11 , November 2016
Klippel-Trenaunay Syndrome: A Rare Cause of Vaginal Bleeding in the Prepubescent Girl
Abstract: Klippel-Trénaunay syndrome (KTS) is an uncommon congenital disorder with unknown etiology that consists of mixed vascular malformations. Visceral organs may also be involved leading to a variety of manifestations. Although seemingly uncommon, genital tract involvement can occur and be a source of significant morbidity. We hereby describe a case of KTS of a 7-year-old female patient presenting with genital bleeding, large venous and capillary malformations and soft tissue hypertrophy of right limb. Patient was treated conservatively and asked to follow-up regularly. KTS should be kept on mind as a cause of vaginal bleeding in preteen girls especially those with suggestive clinical features. Management of this complex condition is challenging because of its progressive nature and wide range of disease severity.
Cite this paper: Essabar, L. , Amenzouy, S. , Oudghiri, F. , Kerboubi, L. and Dakhama, B. (2016) Klippel-Trenaunay Syndrome: A Rare Cause of Vaginal Bleeding in the Prepubescent Girl. Journal of Biosciences and Medicines, 4, 1-7. doi: 10.4236/jbm.2016.411001.
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