ABSTRACT Congenital disorders of glycosylation (CDGs) are group group of genetic defects in the assembly and processing pathway of protein glycosylation, which cause a wide range of multi system dysfunction. This paper describes the anesthetic management of 6 year old boy with CDG type I-x for upper airway surgery. We used a sevoflurane-nitrous oxide-remifentanil regime with no complications and good results. As for now, the literature lacks reports of anesthetic management of children with CDG I-x, and this report may provide clinicians an option for safe anesthetic management.
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nullA. Lehavi, H. Mandel and Y. Katz, "Anesthetic Management of a Boy with Congenital Disorder of Glycosylation (CDG) I-x," International Journal of Clinical Medicine, Vol. 2 No. 3, 2011, pp. 325-327. doi: 10.4236/ijcm.2011.23056.
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