IJOHNS  Vol.4 No.6 , November 2015
A Pierre Robin Syndrome with Absent Anterior 2/3 Tongue—A Case Report
ABSTRACT
The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small and symmetrical receded mandible), glossoptosis (tongue of variable size falls backwards into the post pharyngeal wall), and cleft palate (U or V shaped). We report a case of 2 hours old newborn presented with micrognathia, retrognathia, and glossoptosis and absent anterior two thirds of tongue.

Cite this paper
Surender, K. , Vasudev, K. , Balaram, B. , Vijay Raj, C. and Jadi, L. (2015) A Pierre Robin Syndrome with Absent Anterior 2/3 Tongue—A Case Report. International Journal of Otolaryngology and Head & Neck Surgery, 4, 417-422. doi: 10.4236/ijohns.2015.46067.
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