K. Surender¹, K. Vasudev¹, B. Balaram¹, C. H. Vijay Raj¹, Lingaiah Jadi²

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¹ Department of Pediatrics, Kakatiya Medical College, MGM Hospital, Warangal, India.
² Department of ENT & HNS, Chalmeda Anand Rao Institute of Medical Sciences, Karimnagar, India.
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Abstract: The triad of micrognathia, glossoptosis and airway obstruction originally described in 1923 by Pierre Robin, is known as Robin sequence (or Pierre robin sequence “PRS”). PRS is characterized by micrognathia (small and symmetrical receded mandible), glossoptosis (tongue of variable size falls backwards into the post pharyngeal wall), and cleft palate (U or V shaped). We report a case of 2 hours old newborn presented with micrognathia, retrognathia, and glossoptosis and absent anterior two thirds of tongue.

Keywords: Micrognathia, Glossoptosis, Pierre Robin Sequence

Cite this paper: Surender, K. , Vasudev, K. , Balaram, B. , Vijay Raj, C. and Jadi, L. (2015) A Pierre Robin Syndrome with Absent Anterior 2/3 Tongue—A Case Report. International Journal of Otolaryngology and Head & Neck Surgery, 4, 417-422. doi: 10.4236/ijohns.2015.46067.

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