IJOHNS  Vol.4 No.4 , July 2015
Carotid Artery Prolapse and Myringocarotidopexy in Osteogenesis Imperfecta
ABSTRACT
Osteogenesis Imperfecta is a rare genetic disorder of connective tissue that is caused by an error in collagen formation. The disease is characterized by abnormal bone fragility, osteopenia, blue discoloration of the sclerae and hearing loss. Chronic non-suppurative otitis media is frequent in Osteogenesis Imperfecta patients and usually attributed to Eustachian tube dysfunction due to cranial molding and deformities. In some cases of severe Osteogenesis Imperfecta, the fragile bone of the petrous carotid canal can be broken down by the pulsations of the carotid artery, this may result in prolapse of the carotid artery into the protympanum with resultant Eustachian tube obstruction and tympanic membrane retraction with adhesion to prolapsed carotid artery, a condition called myringocarotidopexy.

Cite this paper
Abdulkarim, H. , Haidar, H. , Abualsoud, A. , Elsotouhy, A. and Alqahtani, A. (2015) Carotid Artery Prolapse and Myringocarotidopexy in Osteogenesis Imperfecta. International Journal of Otolaryngology and Head & Neck Surgery, 4, 286-289. doi: 10.4236/ijohns.2015.44049.
References
[1]   Carey, M.C., Fitzgerald, O. and McKiernan, E. (1968) Osteogenesis Imperfecta in Twenty Three Members of a Kindred with Heritable Features Contributed by a Non-Specific Skeletal Disorder. Quarterly Journal of Medicine, 37, 437-449.

[2]   Stoller, F.M. (1962) The Ear in Osteogenesis Imperfecta. Laryngoscope, 72, 855-869.
http://dx.doi.org/10.1288/00005537-196207000-00002

[3]   Carruth, J.A., Lutman, M.E. and Stephens, S.D. (1978) An Audiological Investigation of Osteogenesis Imperfecta. The Journal of Laryngology & Otology, 92, 853-860.
http://dx.doi.org/10.1017/S0022215100086229

[4]   Cox, J.R. and Simmons, C.L. (1982) Osteogenesis Imperfecta and Associated Hearing Loss in Five Kindreds. Southern Medical Journal, 75, 1222-1226.
http://dx.doi.org/10.1097/00007611-198210000-00016

[5]   Quisling, R.W., Moore, G.R., Jahrsdoerfer, R.A. and Cantrell, R.W. (1979) Osteogenesis Imperfecta: A Study of 160 Family Members. Archives of Otolaryngology, 105, 207-211.
http://dx.doi.org/10.1001/archotol.1979.00790160041011

[6]   Kuurila, K., Kaitila, I., Johansson, R. and Grenman, R. (2002) Hearing Loss in Finnish Adults with Osteogenesis Imperfecta: A Nationwide Survey. Annals of Otology, Rhinology & Laryngology, 111, 939-946.
http://dx.doi.org/10.1177/000348940211101014

[7]   Pedersen, U. (1984) Hearing Loss in Patients with Osteogenesis Imperfecta. A Clinical and Audiological Study of 201 Patients. Scandinavian Audiology, 13, 67-74.
http://dx.doi.org/10.3109/01050398409043042

[8]   Stewart, E.J. and O’Reilly, B.F. (1989) A Clinical and Audiological Investigation of Osteogenesis Imperfecta. Clinical Otolaryngology & Allied Sciences, 14, 509-514.
http://dx.doi.org/10.1111/j.1365-2273.1989.tb00414.x

[9]   Berger, G., Hawke, M., Johnson, A. and Proops, D. (1985) Histopathology of the Temporal Bone in Osteogenesis Imperfecta Congenita: A Report of 5 Cases. Laryngoscope, 95, 193-199.
http://dx.doi.org/10.1288/00005537-198502000-00014

 
 
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