IJOHNS  Vol.4 No.3 , May 2015
Complete Fusion of the Maxillamandibular: Report of a Rare Case and Review of the Literature
ABSTRACT
The maxillomandibular fusion is a very rare condition, with no more than forty cases described in the literature. Adhesions of bone and/or soft tissue between the mandible and maxilla manifest themselves in the inability to open the mouth added to impacts on mandibular growth, nutrition and speech. This condition can be isolated or, when congenital, associated with other anomalies such as cleft lip and palate, aglossia, or Van der Woude syndrome. In the present paper, we report a case of maxillomandibular fusion treated in our department at University Hospital, between February 2011 and June 2014. The case is a congenital maxillomandibular fusion in a two-year-old infant, associated with a syndrome of Van der Woude. We discuss the diagnostic and treatment difficulties on the anaesthetic and surgical levels and the action to be taken to avoid recurrence. To date, some classifications have been suggested in the literature, but there is no standard treatment protocol. Early treatment is necessary to allow freedom of the upper airway, and ensure proper nutrition and good growth of facial bones. The success of surgery is conditioned by an adequate physiotherapy follow-up likely to guarantee the non-recurrence of the lesion.

Cite this paper
Chabbak, H. , Rafik, A. and Chlihi, A. (2015) Complete Fusion of the Maxillamandibular: Report of a Rare Case and Review of the Literature. International Journal of Otolaryngology and Head & Neck Surgery, 4, 220-223. doi: 10.4236/ijohns.2015.43037.
References
[1]   Daniels, J.S. (2004) Congenital Maxillomandibular Fusion: A Case Report and Review of the Literature. Journal of Cranio-Maxillofacial Surgery, 32, 135-139.
http://dx.doi.org/10.1016/j.jcms.2004.01.005

[2]   Burket, L. (1936) Congenital Bony Ankylosis and Facial Hemiatrophy. The Journal of the American Medical Association, 106,1719-1722.

[3]   Laster, Z., Temkin, D., Zarfin, Y. and Kushnir, A. (2001) Complete Bony Fusion of the Mandible to the Zygomatic Complex and Maxillary Tuberosity: Case Report and Review. International Journal of Oral and Maxillofacial Surgery, 30, 75-79.
http://dx.doi.org/10.1054/ijom.2000.0009

[4]   Hegab, A., ElMadawy, A. and Shawkat, W.M. (2012) Congenital Maxillomandibular Fusion: A Report of Three Cases. International Journal of Oral and Maxillofacial Surgery, 41, 1248-1252.
http://dx.doi.org/10.1016/j.ijom.2012.05.004

[5]   Dawson, K.H., Gruss, J.S. and Myall, R.W. (1997) Congenital Bony Syngnathia: A Proposed Classification. The Cleft Palate-Craniofacial Journal, 34, 141-146.
http://dx.doi.org/10.1597/1545-1569(1997)034<0141:CBSAPC>2.3.CO;2

[6]   Miskinyar, S.A. (1979) Congenital Mandibulo-Maxillary Fusion. Plastic and Reconstructive Surgery, 63, 120-121.
http://dx.doi.org/10.1097/00006534-197901000-00029

[7]   Nwoku, A.L. and Kekere-Ekun, T.A. (1986) Congenital Ankylosis of the Mandible: Report of a Case Noted at Birth. Journal of Maxillofacial Surgery, 14, 150-152.
http://dx.doi.org/10.1016/S0301-0503(86)80281-8

[8]   Rao, S., Oak, S., Wagh, M. and Kulkarni, B. (1997) Congenital Midline Palatomandibular Bony Fusion with a Mandibular Cleft and a Bifid Tongue. British Journal of Plastic Surgery, 50, 139-141.
http://dx.doi.org/10.1016/S0007-1226(97)91328-X

[9]   Mortazavi, S.H. and Motamedi, M.H. (2007) Congenital Fusion of the Jaws. Indian Journal of Pediatrics, 74, 416-418.

[10]   Bozdag, S., Erdeve, O., Konas, E., Tuncbilek, G. and Dilmen, U. (2011) Management of Serious Isolated Gingival Synechia in a Newborn: Case Report and Review of the Literature. International Journal of Oral and Maxillofacial Surgery, 40, 1428-1431.
http://dx.doi.org/10.1016/j.ijom.2011.05.003

 
 
Top