Yoshihiro Morita^1,2,3, Kyoko Naito¹, Natsuko Kimoto², Eiji Kimoto², Tetsuji Omata², Nobuo Morita⁴, Masashi Nakagawa^1*

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¹ Department of Anesthesiology, Kinan Hospital, Tanabe, Japan.
² Department of Oral and Maxillofacial Surgery, Kinan Hospital, Tanabe, Japan.
³ Department of Oral and Maxillofacial Surgery, Seichokai Hannan Municipal Hospital, Han-nan, Japan.
⁴ Department of Oral and Maxillofacial Surgery, NS Medical & Healthcare Service General Incorporation Foundation, Wakayama, Japan.
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Abstract: Simpson-Golabi-Behmel syndrome (SGBS) is an X-linked recessive condition associated with pre-natal and postnatal overgrowth with visceral and skeletal anomalies. Abnormal airway anatomy may complicate the perioperative management of SGBS. However, there have been few reports regarding the anesthetic management of children with SGBS. We present the preoperative evalua-tion and intraoperative management of a 1.5-year-old child with SGBS undergoing plastic surgery for cleft palate. Sevoflurane-fentanyl anesthesia without a neuromuscular blocker was planned, due to the preoperative evaluation that airway management would be complicated by the macroglossia and short neck characteristic of SGBS. Fortunately, there was no difficulty in endotracheal intubation in the present patient due to careful planning of general anesthesia and meticulous airway management. Appropriate preoperative preparation for a difficult airway by the anesthe-siologist can ameliorate the difficulties inherent to the anesthetic management of patients with SGBS.

Keywords: Simpson-Golabi-Behmel Syndrome, Anesthetic Management, Macroglossia

Cite this paper: Morita, Y. , Naito, K. , Kimoto, N. , Kimoto, E. , Omata, T. , Morita, N. and Nakagawa, M. (2015) Anesthetic Management of a Child with Simpson-Golabi-Behmel Syndrome—A Case Report. Open Journal of Anesthesiology, 5, 23-26. doi: 10.4236/ojanes.2015.52005.

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