Our Experience with Embryonal Rhabdomyosarcoma Presenting as Aural Polyp
Author(s)
Anoop Attakkil,
Vandana Thorawade,
Mohan Jagade,
Rajesh Kar,
Dnyaneswar Rohe,
Reshma Hanowate,
Devkumar Rangaraja,
Kartik Parelkar
ABSTRACT
Aural polyps are a common clinical entity encountered by otorhinolaryngologist in daily practice. Polyps are frequently seen in paediatric patients, usually inflammatory in nature. In children rhabdomyosarcomas (RMS) can mimic all the cinical features of chronic suppurative otitis media which usually present as external auditory canal mass or polyp. Here we present a case where a male child presented with recurrence of polyp in left ear which was finally diagnosed as embryonal rhabdomyosarcoma which is a rare and invariably fatal disease in children. Through this article we intend to highlight the failures and delay committed in attaining diagnosis in this patient in spite of multispecialty evaluation involving repeated imaging and histopathological correlation. Our experience with embryonal rhabdomyosarcoma throws light on the high vigilance required in handling the aural polyps in pediatric population as early diagnosis and treatment are the key elements for successful outcomes.
Aural polyps are a common clinical entity encountered by otorhinolaryngologist in daily practice. Polyps are frequently seen in paediatric patients, usually inflammatory in nature. In children rhabdomyosarcomas (RMS) can mimic all the cinical features of chronic suppurative otitis media which usually present as external auditory canal mass or polyp. Here we present a case where a male child presented with recurrence of polyp in left ear which was finally diagnosed as embryonal rhabdomyosarcoma which is a rare and invariably fatal disease in children. Through this article we intend to highlight the failures and delay committed in attaining diagnosis in this patient in spite of multispecialty evaluation involving repeated imaging and histopathological correlation. Our experience with embryonal rhabdomyosarcoma throws light on the high vigilance required in handling the aural polyps in pediatric population as early diagnosis and treatment are the key elements for successful outcomes.
Cite this paper
Attakkil, A. , Thorawade, V. , Jagade, M. , Kar, R. , Rohe, D. , Hanowate, R. , Rangaraja, D. and Parelkar, K. (2015) Our Experience with Embryonal Rhabdomyosarcoma Presenting as Aural Polyp. International Journal of Otolaryngology and Head & Neck Surgery, 4, 1-5. doi: 10.4236/ijohns.2015.41001.
Attakkil, A. , Thorawade, V. , Jagade, M. , Kar, R. , Rohe, D. , Hanowate, R. , Rangaraja, D. and Parelkar, K. (2015) Our Experience with Embryonal Rhabdomyosarcoma Presenting as Aural Polyp. International Journal of Otolaryngology and Head & Neck Surgery, 4, 1-5. doi: 10.4236/ijohns.2015.41001.
References
[1] Decker, B.C., Gulya, A.J. and Glasscock, M.E. (2003) Glasscock-Shambaugh Surgery of the Ear. Vol. 1, 5th Edition, PMPH, 353-755. [2] Carol, J.M. and Richard, J.H. (2010) Pediatric Head and Neck Malignancies. In: Paul, W.F., Ed., Cummings Otolarymgology Head & Neck Surgery, Vol. 3, Mosby, Philadelphia, 2835-2849. [3] Chao, C.K., Sheen, T.S., Shau, W.Y., Ting, L.L. and Hsu, M.M. (1999) Treatment, Outcomes, and Prognostic Factors of Ear Cancer. Journal of the Formosan Medical Association, 98, 314-318. [4] Bambakidis, N.C., Megerian, C.A. and Spetzler, R.F. (2009) Surgery of the Cerebellopontine Angle. PMPH USA Ltd., 261-262. [5] Potter, G. (1966) Embryonal Rhabdomyosarcoma of the Middle Ear in Children. Cancer, 19, 221-226.
http://dx.doi.org/10.1002/1097-0142(196602)19:2<221::AID-CNCR2820190213>3.0.CO;2-G [6] Barnes, L. (2005) Pathology and Genetics of Head and Neck Tumours IARC. WHO Classification of Tumours Series, Volume 9 of World Health Organization Classification of Tumours, IARC Press, 335. [7] http://www.cancer.org/acs/groups/cid/documents/webcontent/003136-pdf.pdf [8] Parham, D.M. and Ellison, D.A. (2006) Rhabdomyosarcomas in Adults and Children. An Update. Archives of Pathology Laboratory Medicine, 130, 1454-1465
[1] Decker, B.C., Gulya, A.J. and Glasscock, M.E. (2003) Glasscock-Shambaugh Surgery of the Ear. Vol. 1, 5th Edition, PMPH, 353-755. [2] Carol, J.M. and Richard, J.H. (2010) Pediatric Head and Neck Malignancies. In: Paul, W.F., Ed., Cummings Otolarymgology Head & Neck Surgery, Vol. 3, Mosby, Philadelphia, 2835-2849. [3] Chao, C.K., Sheen, T.S., Shau, W.Y., Ting, L.L. and Hsu, M.M. (1999) Treatment, Outcomes, and Prognostic Factors of Ear Cancer. Journal of the Formosan Medical Association, 98, 314-318. [4] Bambakidis, N.C., Megerian, C.A. and Spetzler, R.F. (2009) Surgery of the Cerebellopontine Angle. PMPH USA Ltd., 261-262. [5] Potter, G. (1966) Embryonal Rhabdomyosarcoma of the Middle Ear in Children. Cancer, 19, 221-226.
http://dx.doi.org/10.1002/1097-0142(196602)19:2<221::AID-CNCR2820190213>3.0.CO;2-G [6] Barnes, L. (2005) Pathology and Genetics of Head and Neck Tumours IARC. WHO Classification of Tumours Series, Volume 9 of World Health Organization Classification of Tumours, IARC Press, 335. [7] http://www.cancer.org/acs/groups/cid/documents/webcontent/003136-pdf.pdf [8] Parham, D.M. and Ellison, D.A. (2006) Rhabdomyosarcomas in Adults and Children. An Update. Archives of Pathology Laboratory Medicine, 130, 1454-1465