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 JBM  Vol.2 No.8 , October 2014
Lymphomatoid Granulomatosis as a Debut of Common Variable Immunodeficiency: A Case Report and Review of Literature
Magdalena Fernández-García1*, Tetyana Zhuravetska2, Jose Luis Rodríguez3, Elsa Ots2
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Abstract: Lymphomatoid granulomatosis, currently called as extranodal angiocentric and angiodestructive immunoproliferative disorder, is a rare entity of unclear etiology. It involves most frequently lungs, central nervous system and skin. The clinical course is variable, but mortality is high. Today, it represents a diagnostic challenge because it can emulate autoimmunity, infection, and malignancy processes. Optimal therapy scheme is still unknown. We report the case of a 20 year-old man presenting with fever, weight loss, sweating, multiple bilateral lung nodules on the chest X-ray and cutaneous involvement.
Keywords: Lymphomatoid Granulomatosis, Common Variable Immunodeficiency, Epstein-Barr Virus
Cite this paper: Fernández-García, M. , Zhuravetska, T. , Rodríguez, J. and Ots, E. (2014) Lymphomatoid Granulomatosis as a Debut of Common Variable Immunodeficiency: A Case Report and Review of Literature. Journal of Biosciences and Medicines, 2, 13-15. doi: 10.4236/jbm.2014.28002.
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