CRCM  Vol.3 No.6 , June 2014
Case Report: Propriospinal Myoclonus
Abstract: This report presents a case of propriospinal myoclonus (PSM) in a previously fit and well female patient who presented with truncal jerking movements when relaxed. Propriospinal myoclonus is a rare condition, of which 80% of the aetiology is idiopathic. It is characterised by involuntary jerking movements of the trunk due to spreading activity via intrinsic propriospinal pathways along the spinal cord. Polymyography is mandatory in the diagnosis of priopriospinal myoclonus however in discerning the differential diagnoses it is inferior to magnetic resonance diffusion tensor imaging. The management of propriospinal myoclonus is dependent on aetiology. Clonazepam has been shown to be effective in the treatment of idiopathic PSM for symptomatic relief.
Cite this paper: Smith, C. and Ramtahal, J. (2014) Case Report: Propriospinal Myoclonus. Case Reports in Clinical Medicine, 3, 364-366. doi: 10.4236/crcm.2014.36081.

[1]   Lozsadi, D. (2012) Myoclonus: A Pragmatic Approach. Practical Neurology, 12, 215-224.

[2]   Zamidei, L., Bandini, M., Michelagnoli, G., Campostrini, R. and Consales, G. (2010) Propriospinal Myoclonus Following Intrathecal Bupivacaine in Hip Surgery: A Case Report. Minerva Anestesiologica, 76, 290-293.

[3]   Bhidayasiri, R. and Tarsy, D. (2012) Propriospinal Myoclonus. Current Clinical Neurology, 26, 192-193.

[4]   Roze, E., Bounolleau, P., Ducreux, D., et al. (2009) Propriospinal Myoclonus Revisited. Neurology, 72, 1301-1309.

[5]   Brown, P., Thompson, P.D., Rothwell, J.C., Day, B.L. and Marsden, C.D. (1991) Axial Myoclonus of Propriospinal Origin. Brain, 114, 197-214.

[6]   Van der Salm, S.M.A., Koelman, J.H.T.M., Henneke, S., van Rootselaar, A. and Tijssen, M.A.J. (2010) Axial Jerks: A Clinical Spectrum Ranging from Propriospinal to Psychogenic Myoclonus. Journal of Neurology, 257, 1349-1355.

[7]   Erro, R., Bhatia, K.P., Edwards, M.J., Farmer, S.F. and Cordivari, C. (2013) Clinical Diagnosis of Propriospinal Myoclonus Is Unreliable: An Electrophysiologic Study. Movement Disorders, 28, 1868-1873.

[8]   Suk, Y., Kang, M.D., Young, H. and Sohn, M.D. (2006) Electromyography Patterns of Propriospinal Myoclonus Can Be Mimicked Voluntarily. Movement Disorders, 21, 1241-1244.

[9]   Gupta, A. and Lang, A.E. (2009) Psychogenic Movement Disorders. Current Opinion in Neurology, 22, 430-436.

[10]   Roze, E., Apartis, E., Vidailhet, M., et al. (2007) Propriospinal Myoclonus: Utility of Magnetic Resonance Diffusion Tensor Imaging and Fiber Tracking. Movement Disorders, 22, 1506-1509.

[11]   Wooyoung, J., Joong-Seok, K., Jin Young, A. and Hee-Tae, K. (2012) Reversible Propriospinal Myoclonus Due to Thoracic Disc Herniation: Long-Term Follow-Up. Journal of the Neurological Sciences, 313, 32-34.

[12]   Maltete, D., Verdure, P., Roze, E., et al. (2008) TENS for the Treatment of Propriospinal Myoclonus. Movement Disorders, 23, 2256-2257.