(HL) is a congenital anomaly and histologically benign tumor, which was
composed of both the lymphatic and the blood vessels. We report an adult case
of HL complicated by chronic thromboembolic pulmonary hypertension (CTEPH) in
a 20-year-old female. Gastrointestinal bleeding
scintigraphy and operative findings elucidate a close relationship between CTEPH and residual HL. This case indicates
that HL survivors with remaining
left-to-right shunt might lead to CTEPH
during the long-term follow-up.
Cite this paper
Nakamura, T. , Tamanuki, K. , Ko, G. , Oguri, M. , Akita, C. , Kitaoka, C. , Nakamura, T. and Saikawa, Y. (2014) Chronic thromboembolic pulmonary hypertension related to hemangiolymphangioma. Case Reports in Clinical Medicine
, 36-37. doi: 10.4236/crcm.2014.31009
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