CRCM  Vol.3 No.1 , January 2014
Chronic thromboembolic pulmonary hypertension related to hemangiolymphangioma
Abstract: Hemangiolymphangioma (HL) is a congenital anomaly and histologically benign tumor, which was composed of both the lymphatic and the blood vessels. We report an adult case of HL complicated by chronic thromboembolic pulmonary hypertension (CTEPH) in a 20-year-old female. Gastrointestinal bleeding scintigraphy and operative findings elucidate a close relationship between CTEPH and residual HL. This case indicates that HL survivors with remaining left-to-right shunt might lead to CTEPH during the long-term follow-up.
Cite this paper: Nakamura, T. , Tamanuki, K. , Ko, G. , Oguri, M. , Akita, C. , Kitaoka, C. , Nakamura, T. and Saikawa, Y. (2014) Chronic thromboembolic pulmonary hypertension related to hemangiolymphangioma. Case Reports in Clinical Medicine, 3, 36-37. doi: 10.4236/crcm.2014.31009.

[1]   Shetty, D.C., Urs, A.B., Rai, H.C., Ahuja, N. and Manchanda, A. (2010) Case series on vascular malformation and their review with regard to terminology and categorization. Contemporary Clinical Dentistry, 1, 259-262.

[2]   Senoh, D., Hanaoka, U., Tanaka, Y., Tanaka, H., Hayashi, K., Yanagihara, T. and Hata, T. (2001) Antenatal ultrasonographic features of fetal giant hemangiolymphangioma. Ultrasound in Obstetrics & Gynecology, 17, 252-254.

[3]   Chandna, S., Bhatnagar, V., Mitra, D.K. and Upadhyaya, P. (1987) Hemangiolymphangioma of the urinary bladder in a child. Journal of Pediatric Surgery, 22, 1051-1052.

[4]   Campos, M., Ortiz, V., Correa, M.S., Santiago B.P.J., Garcia, I., Garcia, L. and Valcárcel, M. (2008) Evidenced based management of neonatal hemangiolymphangioma: A case report. Boletín de la Asociación Médica de Puerto Rico, 100, 57-59.

[5]   McNeil, K. and Dunning, J. (2007) Chronic thromboembolic pulmonary hypertension (CTEPH). Heart, 93, 1152-1158.

[6]   Ozkur, A., Kervancioglu, S., Kervancioglu, R., Dikensoy, E., Inaloz, H.S. and Sirikci, A. (2007) Prenatal sonographic diagnosis of an extensive fetal axillary hemangiolymphangioma. Journal of Clinical Ultrasound, 35, 274-276.

[7]   Zacharia, T.T., Ittoop, A., Perumpillichira, J.J. and Chavhan, G. (2003) Sonographic appearance of a congenital parotid gland hemangiolymphangioma simulating malignancy in an infant. Journal of Clinical Ultrasound, 31, 493-496.

[8]   Rotas, M., Haberman, S., Merhi, Z.O. and Morcos, M. (2006) Prenatal diagnosis of giant fetal truncalhemangioma by means of 2- and 3-dimensional sonography with magnetic resonance imaging. Journal of Ultrasound in Medicine, 25, 527-531.