Cor-triatriatum dexter with pulmonary hypertension in a neonate

Bijay Kumar  Meher; Pradeep  S; Leena  Das; Priyadarsi  Tripathy

doi:10.4236/ojped.2013.34060

Bijay Kumar Meher, Pradeep S, Leena Das, Priyadarsi Tripathy

Abstract: Cor-triatriatum dexter is an extremely rare congenital anomaly, in which right atrium is divided into 2 halves by a septum giving rise to 3 atrial chambers. We report here a case of cor-triatriatum dexter who presented at 3 days of life with tachypnea and did not respond to antibiotics. Echocardiography revealed ostium secundum atrial septal defect (ASD) with right to left flow, intact interventricular septum (IVS), severe tricuspid regurgitation with pulmonary arterial hypertension and a membranous structure dividing right atrium into 2 halves with good biventricular function. The patient improved with sildenafil and anti-failure medication. This case of cor-triatriatum dexter presenting with pulmonary hypertension, tricuspid regurgitation and ASD added to the new spectrum of cor-triatriatum dexter.

Keywords: Cor-Triatriatum; Pulmonary Hypertension; Neonate

Cite this paper: Meher, B. , S, P. , Das, L. and Tripathy, P. (2013) Cor-triatriatum dexter with pulmonary hypertension in a neonate. Open Journal of Pediatrics, 3, 337-339. doi: 10.4236/ojped.2013.34060.

References

[1] Alboliras, E.T., Edwards, W.D., Driscoll, D.J. and Seward, J.B. (1987) Cor triatriatum dexter: Two-dimensional echocardiographic diagnosis. Journal of the American College of Cardiology, 9, 334-337. http://dx.doi.org/10.1016/S0735-1097(87)80385-6

[2] Ahmad, R., Mohd, Z., Koh, G.T. and Sharifah, A. (2012) Cor triatriatum dexter: A rare cause of childhood cyanosis. Annals of Pediatric Cardiology, 5, 92-94. http://dx.doi.org/10.4103/0974-2069.93725

[3] Hansing, C.E., Young, W.P. and Rowe, G.G. (1972) Cor triatriatum dexter. Persistent right sinus venosus valve. American Journal of Cardiology, 30, 559-564. http://dx.doi.org/10.1016/0002-9149(72)90050-1

[4] Burton, D.A., Chin, A., Weinberg, P.M. and Pigott, J.D. (1987) Identification of Cor triatriatum dexter by twodimensional echocardiography. American Journal of Cardiology, 60, 409-410.
http://dx.doi.org/10.1016/0002-9149(87)90268-2

[5] Savas, V., Samyn, J., Schreiber, T.L., Hauser, A. and O’Neill, W.W. (1991) Cor triatriatum dexter: Recognition and percutaneous Trans luminal correction. Catheterization and Cardiovascular Diagnosis, 23, 183-186. http://dx.doi.org/10.1002/ccd.1810230308

[6] Lengyel, M., Arvay, A. and Biro, V. (1987) Two-dimensional echocardiographic diagnosis of Cor triatriatum. American Journal of Cardiology, 59, 484-485. http://dx.doi.org/10.1016/0002-9149 (87)90964-7

[7] Ott, D.A., Cooley, D.A., Angelini, P. and Leachman, R.D. (1979) Successful surgical correction of symptomatic Cor triatriatum dexter. Journal of Thoracic and Cardiovascular Surgery, 78, 573-575.

[8] Choudhary, D., Sivasankaran, S., Venkateshwaran, S. and Sasidharan, B. (2013) Cor triatiratum dexter: A rare cause of isolated right atrial enlargement. Pediatric Cardiology, 34, 198-199. http://dx.doi.org/10.1007/s00246-012-0443-0

[9] Galli, M.A., Galletti, L., Schena, F., Salvini, L., Mosca, F. and Danzi, G.B. (2009) A rare case of neonatal cyanosis due “cor triatriatum dexter” and a review of the literature. Journal of Cardiovascular Medicin (Hagerstown), 10, 535-538. http://dx.doi.org/10.2459/JCM.0b013e32832a574f