CRCM  Vol.2 No.4 , July 2013
Clear cell sarcoma of the jejunum—Surgical management in two patients with review of the literature
ABSTRACT

Clear cell sarcoma is usually described as a malignant melanoma of the soft tissues. The overall prognosis is poor because of delay in diagnosis and vague clinical symptoms. It is rarely involved in the gastrointestinal tract, and its diagnosis is often missed secondary to infrequent occurrence and histological resemblance to melanoma. We present two cases of primary CCS of the jejunum whose clinical presentations were complicated by lymph node involvement. Prompt diagnosis and potential aggressive surgical intervention may improve overall survival.


Cite this paper
Mehta, A. , Brownson, K. , Massarani, R. , Esposito, T. , Abood, G. and Shoup, M. (2013) Clear cell sarcoma of the jejunum—Surgical management in two patients with review of the literature. Case Reports in Clinical Medicine, 2, 272-276. doi: 10.4236/crcm.2013.24074.
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