AMI  Vol.3 No.2 , April 2013
Malignant Triton Tumor in the Abdominal Wall: A Case Report
ABSTRACT

Malignant triton tumor (MTT) is a rare variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. We report the case of a 54-year-old male without a history of neurofibromatosis type 1 (NF1) who had a growing abdominal wall tumor diagnosed as MTT. Computed tomography (CT), magnetic resonance imaging (MRI) and 2-[F-18]-fluoro-2-deoxy-D-glucose positron emission tomography/CT (FDG-PET/CT) were performed. The MRI and FDG-PET/CT indicated that the lateral component of the tumor was composed of many proliferative cells, corresponding to the histopathological finding of a cellular proliferation of spindle-shaped cells. In light of this case and previous reports, it is apparent that FDG-PET/CT is a helpful tool for distinguishing MTT from benign peripheral nerve sheath tumor.


Cite this paper
Y. Kitamura, K. Abe, S. Baba, T. Isoda, Y. Maruoka, Y. Matsuo, Y. Kubo, A. Sakamoto, H. Nishimura, M. Sasaki and H. Honda, "Malignant Triton Tumor in the Abdominal Wall: A Case Report," Advances in Molecular Imaging, Vol. 3 No. 2, 2013, pp. 9-13. doi: 10.4236/ami.2013.32002.
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