OJRA  Vol.2 No.3 , August 2012
Erdheim-Chester Disease with Right Atrial Tumor and “Temporal Arteritis”
Abstract: Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases. We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was success-fully managed with anakinra as anti IL-1 therapy.
Cite this paper: J. Skalski, W. Edwards and E. Matteson, "Erdheim-Chester Disease with Right Atrial Tumor and “Temporal Arteritis”," Open Journal of Rheumatology and Autoimmune Diseases, Vol. 2 No. 3, 2012, pp. 37-38. doi: 10.4236/ojra.2012.23008.

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